Surgery is the treatment of choice with two available options. Fibrous dysplasia of the maxilla jama otolaryngology. Pdf fibrous dysplasia is a rare bone disorder characterized by the replacement of normal bone by abnormal fibrous tissue. Orbital scoringtransposition supraorbital fibrous dysplasia dr. Fibrous dysplasia is a nonneoplastic developmental disease of bone, which manifest as a defect in osteoblastic differentiation and maturation. The frontal process of the maxilla occasionally shows a localized fdlike appearance. Fibrous dysplasia is a rare bone disorder characterized by the replacement of normal bone by abnormal fibrous tissue. Fibrous dysplasia of the mandible fibrous dysplasia report george w. Here we present a 16yearold female with a fibrous dysplasia in the maxilla and obliteration of the sinus in the same side. The etiology of fibrous dysplasia has been linked to an activating mutation in the gene that encodes the.
Pdf radiographic diagnosis of fibrous dysplasia in maxilla. Radiographic diagnosis of fibrous dysplasia in maxilla. Fibrous dysplasia of the mandible pdf free download. Fibrous dysplasia is characterized by excessive proliferation of boneforming mesenchymal cells. It is seen in 2 main forms of presentation, monoostotic and the polyostotic form with cafe au lait spots and precocious puberty mccunealbright. Craniofacial fibrous dysplasia is 1 of 3 types of fibrous dysplasia that can affect the bones of the craniofacial complex, including the mandible and maxilla. The maxilla is the most commonly affected facial bone, with facial asymmetry being the usual complaint.
A retrospective study of consecutive paranasal sinus ct scans was preformed on outpatients without a history of trauma or previous surgery in our hospital during 6 months. Fibrous dysplasialike appearance of the frontal process. Here we present a 16yearold female with a fibrous dysplasia in the maxilla. The purpose of this study was to determine its prevalence and findings on ct. Cone beam computed tomography scan revealed a mixed radiopacity that extended from the alveolar crest of the right posterior teeth to the right orbital. Fibrous dysplasia is a developmental tumor like condition in which normal bone is replaced by excessive proliferation of cellular fibrous connective tissue intermixed with irregular bony trabeculae. It represents with three forms namely monostotic single bone involvement, polyostotic multiple bone.
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